fibrous dysplasia, regional odontodysplasia, gingival fibromatosis, central hemangioma and tumour of bone were considered. Radiographic examination of the ...
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Case Report
Segmental odontomaxillary dysplasia Arti Agrawal, Jonathan Daniel, Vasudevan Vijeev1 Department of Oral Medicine and Radiology, Mahatma Gandhi PostGraduate Institute of Dental Sciences, Pondicherry, Puducherry (UT), 1Department of Oral Medicine and Radiology, Krishnadevaraya Dental College and Hospital, Bengaluru, Karnataka, India
Abstract
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Segmental odontomaxillary dysplasia is a type of hemi-maxillofacial dysplasia. It is a sporadic, mesoectodermal dysplasia that presents early in life, possibly as early as in utero and exhibits male gender predominance (1.7:1.0). Its features include enlargement of the soft tissue and/or bone of one hemimaxilla that may produce mild facial asymmetry, sclerotic radiographic bone changes and dental developmental abnormalities. The dense bone, which often exhibits a radiographic vertical orientation of the trabecular bone pattern, is generally associated with delayed eruption of the teeth. Congenitally missing premolar teeth (either or both) is a common feature of this condition that is of significant diagnostic value. Ipsilateral cutaneous findings have been reported in 23% of cases. Immature woven bone forming irregular patterns are seen histologically. Herein, we present a case report on segmental odontomaxillary dysplasia in a 13-year-old boy.
Keywords: Facial asymmetry, hemimaxillofacial dysplasia, segmental odontomaxillary dysplasia
Introduction Segmental odontomaxillary dysplasia is a rare developmental disorder that causes a unilateral disturbance of the maxilla associated with an abnormal growth and maturation of bone, teeth and adjacent gingival tissue, with or without facial cutaneous lesions.[1] The prevalence of this condition is not well established as the available literature regarding this condition is scanty and largely consists of case reports only.[4] Until date,
